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Published on: February 29, 2020
Chiari Type I Malformation Presenting with Unilateral Hearing Loss
Abdulhamid Ciçek1,2, Jeroen Cortier1, Sarah Hendrickx1
1Department of Neurosurgery, AZ Delta, Roeselare, Belgium.
Introduction:
Chiari type I malformations can present in different ways, but the most frequent symptom is an occipitocervical headache. Hearing loss as the main presenting symptom is rare.
Case:
A young woman with progressive left-sided unilateral hearing loss was diagnosed with a Chiari type I malformation. She underwent a suboccipital craniectomy with C1 laminectomy and duraplasty. The hearing loss had resolved postoperatively with normalization of the audiometry.
Conclusion:
Chiari type I malformation can present solely with hearing loss. Improvement after surgical decompression is possible. This phenomenon is not emphasized well enough within the neurologic community. In this report, we present a summary of the pathophysiology and management in Chiari type I malformations.
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