Impaired Binding to Junctophilin-2 and Nanostructural Alteration in CPVT Mutation

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Liheng Yin1, Alexandra Zahradnikova1, Riccardo Rizzetto1

  • 1Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).

Circulation Research
|June 11, 2021
PubMed

Abstract:

[Figure: see text].

Keywords:
action potentialcalciumjunctophilinmutationryanodine receptorventricular tachycardia

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