Pregnancy and delivery in a patient with a Fontan circulation and primary ciliary dyskinesia: A case report

Sébastien Grandfils1, Pierre-Yves Dewandre2, Pierre Bonnet3

  • 1Department of Gynecology and Obstetrics. CHU of Liege, University Hospital of Liege, 600 Rue de Gaillarmont, Liege 4032, Belgium.

A patient had primary ciliary dyskinesia with a complex cardiac malformation. As a child, she had benefited from a Fontan surgery to maintain a proper cardiac function. In such patients, whether it is safe to become pregnant is controversial. This case illustrates the possibility of carrying a pregnancy to term and providing a vaginal birth if a rigorous preconception consultation is performed to ensure care by a multidisciplinary specialized team, and the patient is properly informed of the risks.

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