Left ventricle implantable cardioverter defibrillator: a dextro-transposition of the great arteries case

Miguel Martins de Carvalho1,2, Raquel Mota Garcia1, Cristina Cruz1

  • 1Department of Cardiology, São João Universitary Hospital, Porto, Portugal.

Insights

A patient with dextro-transposition of the great arteries experienced a long-term arrhythmic complication requiring an Implantable Cardioverter Defibrillator (ICD). This case underscores the need for innovative interventions in complex congenital heart disease management.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Electrophysiology

Background:

  • Dextro-transposition of the great arteries (dTGA) is a complex congenital heart defect.
  • The Senning procedure is a palliative surgical approach for dTGA.
  • Long-term management of palliated dTGA patients can present challenges.

Observation:

  • A patient with dTGA, palliated with a Senning procedure, developed a significant long-term arrhythmic complication.
  • The arrhythmia necessitated an interventional approach.
  • An Implantable Cardioverter Defibrillator (ICD) was implanted in the sub-pulmonary ventricle.

Findings:

  • The case demonstrates a rare but serious arrhythmic complication following Senning palliation for dTGA.
  • Successful intervention with ICD implantation in the morphologically left ventricle was achieved.
  • This highlights the potential for late-onset ventricular dysfunction and arrhythmias.

Implications:

  • Management of long-term complications in complex congenital heart disease requires tailored, often off-label, strategies.
  • Further research into the electrophysiological substrate of palliated dTGA is warranted.
  • This case emphasizes the importance of lifelong cardiac monitoring and management for these patients.

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