Idiopathic intracranial hypertension with juvenile idiopathic arthritis-associated uveitis: A case report

Asaad Alkoht1, Huda Alhariry1, Ibrahem Hanafi2

  • 1Faculty of Medicine Division of Rheumatology Department of Internal Medicine Damascus University Damascus Syria.

Insights

This case study highlights a child with juvenile idiopathic arthritis-associated uveitis who developed idiopathic intracranial hypertension without typical risk factors, suggesting a potential link between these conditions.

Area of Science:

  • Ophthalmology
  • Pediatrics
  • Neurology

Background:

  • Juvenile idiopathic arthritis (JIA) is a common cause of chronic childhood uveitis.
  • Idiopathic intracranial hypertension (IIH) is a neurological condition characterized by increased intracranial pressure without a clear cause.

Observation:

  • A 14-year-old female patient presented with JIA-associated uveitis and optic disc edema.
  • The patient was subsequently diagnosed with IIH.

Findings:

  • This represents the fifth reported pediatric case of coexisting uveitis and IIH.
  • Notably, this patient had no identifiable risk factors typically associated with IIH.

Implications:

  • The findings suggest a potential, though rare, association between JIA-associated uveitis and IIH in children.
  • Further research is warranted to explore the underlying mechanisms and clinical significance of this comorbidity.

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