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Mesenteric fibromatosis with ureteric stenosis
S Hailemariam1, P Jaeger, N Goebel
1Department of Urology, University Hospital, Zurich, Switzerland.
Postgraduate Medical Journal
|January 1, 1988
Summary
A rare intra-abdominal tumor, mesenteric fibromatosis, caused a right hydronephrosis in a 37-year-old man. Surgical resection led to a full recovery, highlighting this neoplasm
Area of Science:
- Gastroenterology and Surgical Oncology
- Abdominal Neoplasms
- Mesenteric Fibromatosis
Background:
- Mesenteric fibromatosis (desmoid tumors) are rare, locally aggressive neoplasms originating from mesenchymal cells.
- Intra-abdominal desmoid tumors can present insidiously, often with non-specific symptoms.
- Differential diagnosis includes other abdominal masses and conditions causing ureteral obstruction.
Observation:
- A 37-year-old male presented with vomiting, colicky abdominal pain, and microscopic hematuria.
- Radiological examination revealed a right hydronephrosis attributed to a paracecal tumor involving the right ureter.
- The patient lacked predisposing factors for desmoid tumors, such as Gardner's syndrome.
Findings:
- Surgical resection of the paracecal tumor was performed.
- Histological examination confirmed the diagnosis of mesenteric fibromatosis.
- The patient exhibited no signs of recurrence or complications eight months post-surgery.
Implications:
- This case underscores the importance of considering rare intra-abdominal neoplasms in the differential diagnosis of obstructive uropathy.
- Complete surgical resection is a viable treatment option for localized mesenteric fibromatosis.
- Further review of literature on intra-abdominal mesenteric fibromatosis is warranted for understanding its behavior and management.