Gigantic arteriovenous fistula between left coronary cusp and coronary sinus draining into the right atrium
Syed Raza Shah1, Imtiaz Ismail2, Munis Raza1
1Cardiology Fellow, University of Louisville, Louisville, KY, USA.
Insights
A rare coronary arteriovenous fistula (CAF), an abnormal connection between coronary arteries and heart chambers, was incidentally found in an asymptomatic man. Medical management and surveillance were recommended due to the patient
Area of Science:
- Cardiology
- Radiology
- Anatomical Pathology
Background:
- Coronary arteriovenous fistulas (CAF) are rare congenital anomalies with an incidence of 0.002%.
- These fistulas create abnormal direct connections between the coronary arteries and cardiac chambers.
- CAF originating from the left coronary artery are exceptionally uncommon.
Purpose of the Study:
- To report a rare case of a gigantic coronary arteriovenous fistula.
- To discuss the incidental diagnosis and management of an asymptomatic patient with CAF.
- To highlight the role of advanced imaging in detecting rare cardiac anomalies.
Main Methods:
- Incidental detection of a gigantic CAF using low-dose Computed Tomography (CT) scan of the chest.
- Multidisciplinary consultation with cardiothoracic surgeons for case review.
- Recommendation for conservative medical management and close surveillance.
Main Results:
- A middle-aged, asymptomatic male patient was diagnosed with a gigantic CAF.
- The fistula was incidentally discovered during a routine low-dose CT scan.
- Conservative management with ongoing surveillance was advised by specialists.
Conclusions:
- Asymptomatic, incidentally discovered gigantic CAF can be managed conservatively with close monitoring.
- Low-dose CT imaging is effective in identifying rare cardiac anomalies like CAF.
- Further research may lead to novel, less invasive therapeutic options for CAF.
Abstract:
Coronary arteriovenous fistulas (CAF) are infrequent anatomic anomalies that establish a direct connection between coronary arteries and cardiac chambers. The reported incidence is extremely low and estimated at 0.002% in the general population. We report a rare case of CAF in a middle-aged man, who was asymptomatic but incidentally found to have a gigantic CAF on a low-dose Computed Tomography scan of his chest. The case was presented to cardiothoracic surgeons. Since the patient was asymptomatic, they recommended medical management and continued close surveillance. The Left Coronary Artery or its branches are extremely uncommon site for CAF. With the advances in technology, the network of veins including coronary sinus has gained further clinical relevance. While technology has helped elucidate many aspects of these rare anomalies, mysteries still remain. With continued research, we can expect more cost-effective and less invasive interventional therapies to be developed in the near future.
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