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Abdominal unicentric Castleman's disease: a case report.
Samir Bradai1, Amal Khsiba1, Abdelwaheb Nakhli1
1Gastroenterology Department, Mohamed Tahar Maamouri Hospital, Nabeul, Tunisia.
The Pan African Medical Journal
|July 21, 2021
Summary
Castleman's disease, a rare lymphoproliferative disorder, can present as a challenging retroperitoneal tumor. This case highlights the importance of considering Castleman's disease in the differential diagnosis of such masses.
Area of Science:
- Oncology
- Pathology
Background:
- Castleman's disease is a rare lymphoproliferative disorder with unicentric and multicentric forms.
- Mediastinal involvement is most common, but intra-abdominal presentations are rare.
Observation:
- A 65-year-old female presented with epigastric pain.
- Imaging revealed a retroperitoneal mass.
Findings:
- The retroperitoneal mass was surgically resected.
- Histopathology confirmed hyaline-vascular type Castleman's disease.
Implications:
- Castleman's disease poses a diagnostic challenge.
- It should be considered in the differential diagnosis of retroperitoneal tumors.

