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Systematic Hearing Performance Evaluation Process for Adolescents with Cochlear Implantation at Early Ages
Published on: March 24, 2023
Cochlear Implant Behavioral Outcomes for Children With Auditory Neuropathy Spectrum Disorder: A Mini-Systematic
Katherine Myers1, Nannette Nicholson1
1Department of Audiology, Nova Southeastern University, Fort Lauderdale, FL.
Insights
Cochlear implants (CIs) benefit children with auditory neuropathy spectrum disorder (ANSD), improving speech, language, and auditory skills. Early implantation before age three yields outcomes comparable to those with sensorineural hearing loss.
Area of Science:
- Audiology
- Speech-Language Pathology
- Pediatric Otolaryngology
Background:
- Auditory Neuropathy Spectrum Disorder (ANSD) presents unique challenges in auditory processing.
- Early intervention with cochlear implants (CIs) is crucial for children with hearing loss.
- Understanding outcomes for ANSD in CI recipients is vital for clinical practice.
Purpose of the Study:
- To systematically review speech, language, and auditory outcomes in children with ANSD who received CIs before age three.
- To evaluate the evidence base for CI effectiveness in this pediatric population.
Main Methods:
- A mini-systematic review of peer-reviewed literature from 2009-2019.
- Searched two databases using a PICO framework.
- Critically appraised four included studies for research design and risk of bias.
Main Results:
- Evidence supports cochlear implantation as an effective intervention for children with ANSD.
- All included studies reported improvements in speech, language, and auditory outcomes.
- Children with ANSD receiving CIs achieved outcomes similar to those with sensorineural hearing loss and CIs.
Conclusions:
- Cochlear implantation is a viable option for children diagnosed with ANSD.
- Early CI intervention can lead to significant improvements in communication abilities.
- Findings inform clinical practice, parent counseling, and set realistic expectations for children with ANSD and CIs.
Abstract:
Objective The aim of this mini-systematic review was to evaluate the evidence reporting speech, language, and auditory behavioral outcome measures for children with a diagnosis of auditory neuropathy spectrum disorder (ANSD) who received cochlear implants (CIs) prior to 3 years of age. Method A mini-systematic review of the literature supporting evidence-based practices was performed. Two databases were searched utilizing a search strategy derived from the PICO (patient, intervention, comparison, outcome) framework. Peer-reviewed articles published between 2009 and 2019 evaluating children with a diagnosis of ANSD who were implanted prior to 3 years of age with a range of speech, language, and auditory behavioral outcomes were included. Four articles meeting inclusion criteria were critically appraised for reputable research design and risks of bias. Each of the four studies was assigned a level of evidence for effectiveness and quality assessment rating. Results Evidence supports cochlear implantation as an appropriate intervention for children with ANSD. Improvements in outcome performance were observed in all the included studies. Children with ANSD fit with CIs can achieve outcomes similar to children with sensorineural hearing loss and CIs, despite the heterogeneity of ANSD. Conclusion These findings have implications for clinical practice and for future research with current CI technology for facilitating parent education, counseling, and realistic expectations for children with ANSD and CIs.
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