Atrial septal defect with Crochetage sign presenting with pulmonary artery thrombosis

Neerusha Kaisbain1, Wei Juan Lim2,3, Heng Shee Kim4

  • 1Department of Medicine, Hospital Sultanah Aminah, Johor Bahru, Johor, Malaysia.

BMJ Case Reports
|July 28, 2021
PubMed

Insights

This study highlights how specific electrocardiogram (ECG) signs, like the Crochetage sign and incomplete right bundle branch block (IRBBB), can aid in diagnosing atrial septal defect (ASD) in adults. Early ECG recognition of ASD is crucial, especially for preventing complications like pulmonary thrombosis in patients with Eisenmenger syndrome.

Area of Science:

  • Cardiology
  • Medical Diagnostics

Background:

  • Atrial septal defect (ASD) is a common congenital heart defect in adults.
  • Electrocardiography (ECG) offers several sensitive findings for ASD diagnosis.

Observation:

  • A 50-year-old male presented with Crochetage sign, incomplete right bundle branch block (IRBBB), and right ventricular strain on ECG.
  • The Crochetage sign is highly specific for ASD and correlates with shunt severity.
  • Combined Crochetage sign and IRBBB patterns increase diagnostic specificity for ASD.

Findings:

  • The patient was diagnosed with a large (3 cm) ASD with a bidirectional shunt.
  • Pulmonary thrombosis was identified concurrently with the large ASD.
  • ECG findings, including Crochetage sign and IRBBB, were crucial for diagnosis.

Implications:

  • High clinical suspicion for ASD, supported by traditional ECG signs, remains vital in contemporary medicine.
  • Patients with Eisenmenger syndrome face an elevated risk of pulmonary thrombosis.
  • Accurate ECG interpretation is essential to differentiate signs like Crochetage from IRBBB abnormalities.

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