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Systematic Hearing Performance Evaluation Process for Adolescents with Cochlear Implantation at Early Ages
Published on: March 24, 2023
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Audiological and Speech Performance After Cochlear Implantation in Cochlear Aplasia Deformity
1College of Medicine, King Abdullah Ear Specialist Center, King Saud University, Riyadh, SAU.
Cureus
|August 2, 2021
Summary
Cochlear implantation can restore hearing in children with inner ear malformations like cochlear aplasia. A one-year follow-up showed significant speech development after unilateral cochlear implantation.
Area of Science:
- Otolaryngology
- Pediatric audiology
- Medical imaging
Background:
- Inner ear malformations are congenital conditions causing prelingual sensorineural hearing loss in children.
- Cochlear aplasia, a specific malformation, presents diagnostic challenges, particularly differentiating cystic subtypes.
Observation:
- This case report details a child with bilateral, radiologically diagnosed cochlear aplasia.
- The child received a unilateral cochlear implant in the left ear.
Findings:
- One year post-surgery, audiological results indicated positive outcomes.
- At 16 months postsurgery, the child had a vocabulary of 200 words and could form two-word sentences.
Implications:
- Cochlear implantation is a viable option for pediatric hearing loss due to inner ear malformations.
- Difficulties in classifying cystic cavities should not prevent cochlear implant trials if the inner ear anatomy is suitable and the cochleovestibular nerve is present.
