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Robotic Cochlear Implantation for Direct Cochlear Access
Published on: June 16, 2022
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Cochlear Implantation in Pierre Robin Syndrome
Shubhangi Gupta1, Mukesh Dagur2, Mohnish Grover1
1Department of ENT, SMS Medical College and Hospital, Jaipur, Rajasthan India.
Summary
Pierre Robin Syndrome can cause congenital hearing loss, often conductive, but sensorineural loss is possible. Early evaluation and interventions like cochlear implants are crucial for managing hearing impairment in affected children.
Area of Science:
- Otolaryngology
- Genetics
- Pediatrics
Background:
- Hereditary hearing loss is a significant cause of deafness, with syndromic forms accounting for a substantial portion.
- Pierre Robin Syndrome is a congenital condition characterized by micrognathia, glossoptosis, and cleft palate, often associated with hearing loss.
Purpose of the Study:
- To present a case of Pierre Robin Syndrome with congenital hearing loss.
- To highlight the audiological manifestations and management of hearing impairment in this syndrome.
Main Methods:
- Case report of a patient with Pierre Robin Syndrome.
- Audiological evaluation, including assessment for middle ear effusion.
- Surgical intervention (cochlear implant) and medical management (antihistamines, steroid spray).
Main Results:
- The patient presented with congenital hearing loss and bilateral serous otitis media.
- Cochlear implantation was performed.
- Medical treatment was initiated for middle ear effusion.
Conclusions:
- Pierre Robin Syndrome is associated with diverse types of hearing loss, necessitating thorough audiological assessment.
- Multifaceted management, including surgical and medical approaches, is vital for addressing hearing deficits in syndromic hearing loss.
