Giant diverticulum of coronary sinus with multiple accessory pathways treated with catheter ablation

Sinem N Selcuk1, İlker Ertugrul1, Tevfik Karagoz1

  • 1Division of Pediatric Cardiology, Department of Pediatrics, Hacettepe University Faculty of Medicine, Ankara, Turkey.

Cardiology in the Young
|September 23, 2021
PubMed

Insights

A rare giant coronary sinus diverticulum in a child was successfully treated with catheter ablation for Wolff-Parkinson-White syndrome. This case highlights effective radiofrequency ablation for complex congenital heart anomalies and arrhythmias.

Area of Science:

  • Cardiology
  • Pediatric Electrophysiology
  • Congenital Heart Disease

Background:

  • Coronary sinus abnormalities can be symptomatic and associated with cardiac arrhythmias.
  • Giant diverticulum of the coronary sinus is a rare congenital anomaly.
  • Wolff-Parkinson-White syndrome is a common cause of supraventricular tachycardia in children.

Purpose of the Study:

  • To report a case of a pediatric patient with a giant coronary sinus diverticulum and Wolff-Parkinson-White syndrome.
  • To describe the successful management of this complex condition using catheter ablation.
  • To highlight the efficacy of radiofrequency ablation in treating accessory pathways associated with coronary sinus anomalies.

Main Methods:

  • A 5-year-old patient with a giant coronary sinus diverticulum and Wolff-Parkinson-White syndrome was identified.
  • Multidrug therapy was initially administered due to inadequate response.
  • Catheter ablation targeting posteroseptal and left posterolateral accessory pathways was performed via the coronary sinus.

Main Results:

  • Radiofrequency ablation through the coronary sinus successfully eliminated the accessory pathways.
  • The patient's arrhythmia disorder was effectively managed post-ablation.
  • Successful treatment of a rare congenital anomaly associated with a significant arrhythmia.

Conclusions:

  • Catheter ablation is a viable and effective treatment for pediatric patients with giant coronary sinus diverticulum and Wolff-Parkinson-White syndrome.
  • Radiofrequency ablation through the coronary sinus can successfully target accessory pathways in complex anatomical variations.
  • This case underscores the importance of considering interventional electrophysiology for managing rare congenital cardiac anomalies presenting with arrhythmias.

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