Coronary Sinus Ostial Obstruction in Single-Ventricle Congenital Heart Disease: Two Patients With Different Outcomes
Stephen T Dalby1,2, William M Mitchell1,2,3, Lawrence E Greiten1,4
1Arkansas Children's Hospital, Little Rock, Arkansas, USA.
JACC. Case Reports
|September 24, 2021
Insights
Coronary sinus ostial obstruction is a rare heart anomaly. Early diagnosis is crucial for single-ventricle patients to improve surgical outcomes.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Coronary sinus ostial obstruction is a rare congenital anomaly.
- Diagnosis is critical in single-ventricle patients prior to surgical palliation.
Observation:
- Presents two cases of coronary sinus ostial obstruction.
- Cases include an infant and an adult patient.
- Demonstrates varied clinical outcomes based on diagnostic timing.
Findings:
- Coronary sinus ostial obstruction can present across different age groups.
- Timely diagnosis significantly impacts patient outcomes.
- Illustrates the importance of pre-operative assessment in complex congenital heart disease.
Implications:
- Highlights the need for vigilance in diagnosing rare cardiac anomalies.
- Emphasizes the role of early detection in optimizing surgical palliation for single-ventricle physiology.
- Suggests potential for improved diagnostic strategies and patient management.
Abstract:
Coronary sinus ostial obstruction is an exceedingly rare anomaly that is particularly important to diagnose in patients with single-ventricle heart disease before surgical palliation. We present 2 cases, an infant and an adult, diagnosed with coronary sinus ostial obstruction, with different clinical outcomes due to timing of diagnosis. (Level of Difficulty: Intermediate.).
Keywords:
CS, coronary sinusCSOO, coronary sinus ostial obstructionLIV, left innominate veinLSVC, left superior vena cavaSCPA, superior cavopulmonary anastomosisTCPA, total cavopulmonary anastomosisadults with congenital heart diseasechildrencongenital heart surgerycoronary sinus obstructioncoronary sinus ostial atresiasingle-ventricle congenital heart diseaseMore Related Videos
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