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Malignant primary pericardial mesothelioma presenting as effusive constrictive pericarditis: a case report study
Amir Savarrakhsh1, Azin Vakilpour1, Sam Zeraatian-Nejad Davani2
1Cardiovascular Diseases Research Center, Department of Cardiology, Heshmat Hospital School of Medicine, Guilan University of Medical Sciences, 15 Khordad Street, District 2, Rasht, Guilan Province, Iran.
Primary pericardial mesothelioma (PPM) is a rare cancer. This case highlights constrictive pericarditis as an unusual presentation, emphasizing diagnostic challenges for this deadly malignancy.
Area of Science:
- Cardiovascular Pathology
- Thoracic Oncology
Background:
- Primary pericardial mesothelioma (PPM) is a rare and aggressive malignancy.
- Diagnosis of PPM is often delayed due to non-specific symptoms and imaging findings.
Observation:
- A 44-year-old woman presented with symptoms initially diagnosed as effusive constrictive pericarditis.
- Imaging revealed thickened pericardium, effusion, and mediastinal mass-like lesions.
- Histopathology post-pericardiectomy confirmed primary pericardial mesothelioma.
Findings:
- Constrictive pericarditis represents an uncommon clinical manifestation of PPM.
- The case underscores the diagnostic complexities associated with this rare cancer.
Implications:
- Increased awareness of PPM in atypical cardiac presentations is crucial for early diagnosis.
- Timely diagnosis and treatment are vital due to the high mortality rate of PPM.
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