A rare presentation of low-grade appendiceal mucinous neoplasm within an amyand's hernia: a case report

Hani Atiqah Saim1, Ian Chik1, Fahrol Fahmy Jaafar1

  • 1Department of Surgery, Universiti Kebangsaan Malaysia Medical Centre, Kuala Lumpur, Malaysia.

Annals of Coloproctology
|October 18, 2021
PubMed

Insights

An incidental Amyand's hernia containing an appendiceal mucocele was found during gallbladder surgery. The mucocele was diagnosed as a rare low-grade appendiceal mucinous neoplasm (LAMN), highlighting the importance of investigating such rare hernia cases.

Area of Science:

  • Gastroenterology
  • Surgical Oncology
  • Abdominal Surgery

Background:

  • Amyand's hernia, defined as the appendix within an inguinal hernia sac, is a rare condition.
  • Appendiceal mucoceles, while uncommon, can range from benign to malignant, necessitating careful diagnosis and management.
  • The co-occurrence of Amyand's hernia and appendiceal mucocele is exceptionally rare.

Observation:

  • A 75-year-old female patient undergoing laparoscopic cholecystectomy incidentally presented with an Amyand's hernia.
  • The hernia sac contained an appendiceal mucocele without signs of perforation.
  • A long-standing right inguinal swelling, previously misdiagnosed as a cyst, was identified as the hernia.

Findings:

  • Histopathological examination revealed the appendiceal mucocele to be a low-grade appendiceal mucinous neoplasm (LAMN).
  • The patient underwent open appendicectomy and tension-free mesh repair for the hernia.
  • The LAMN diagnosis underscores the potential for malignancy in appendiceal mucoceles, even within a hernia.

Implications:

  • This case highlights the diagnostic challenge and potential for malignancy in appendiceal mucoceles associated with Amyand's hernia.
  • Early recognition and appropriate surgical intervention are crucial for managing these rare conditions.
  • Further research into the natural history and optimal treatment strategies for concurrent Amyand's hernia and appendiceal neoplasia is warranted.

Related Concept Videos