[Subtotal sternal agenesis with ectopia cordis: surgical management and long-term outcome (a case in Benin)]
Antoine Séraphin Gbenou1, Abdel-Kémal Bori Bata1, Joseph Akodjènou2
1Service de Chirurgie Pédiatrique du Centre Hospitalier Universitaire de la Mère et de l´Enfant-Lagune, 01 BP 107, Ave Delorme, Cotonou, Bénin.
Abstract:
Sternal agenesis as well as ectopia cordis are extremely rare congenital malformations. We here report a single case treated in the Department of Paediatric Surgery in Benin. The study involved a 3-year-old girl with congenital sternal agenesis associated with ectopia cordis; firstly, she underwent controlled healing. Then thoracoplasty was performed with favourable outcome. Long-term results are good. Now, she is 13 years old, is attending school and has a satisfactory clinical condition. This is one of the few cases reported in the literature. Optimal therapeutic management has been keeping the patient alive in West Africa.
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