Retrobulbar Hemorrhage Secondary to Acquired Hemophilia A

Hishali D Jayasundara1, Lasitha Y Herath1, Keertie S Kularatne1

  • 1Medicine, National Hospital Kandy, Kandy, LKA.

Cureus
|October 18, 2021
PubMed

Acquired hemophilia A (AHA) is a different bleeding disorder to that of classic hemophilia A. It is an autoimmune-mediated bleeding disorder due to the presence of autoantibodies (inhibitors) directed against plasma coagulation factor VIII. This can result in fatal hemorrhage; thus, eradication of the antibody is the mainstay of treatment. Nontraumatic retrobulbar hemorrhage is a very rare presentation of hemophilia. We report an elderly male presenting with retrobulbar hemorrhage secondary to AHA who was successfully treated with immunosuppression.

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