Extra-Axial Cerebello-Pontine Angle Medulloblastoma in an Infant: A Rare Case Report with Review of Literature

Santosh Prabhu1, Sidharth Agarwal1, Sujata Prabhu1

  • 1Department of Neurosurgery, Western India Institute of Neurosciences, Kolhapur, Maharashtra, India.

Insights

Extra-axial cerebellopontine angle medulloblastoma is rare in children. This case report details an 8-month-old infant diagnosed with this rare pediatric brain tumor and discusses its management.

Area of Science:

  • Pediatric neuro-oncology
  • Neurosurgery
  • Pediatric pathology

Background:

  • Medulloblastoma typically presents as an intra-axial cerebellar mass in children.
  • Extra-axial medulloblastoma in the cerebellopontine angle (CPA) is exceptionally rare, with limited reported cases.
  • Infantile cases of extra-axial CPA medulloblastoma are exceedingly uncommon.

Purpose of the Study:

  • To report a rare case of an 8-month-old infant with an extra-axial CPA medulloblastoma.
  • To discuss the diagnostic and management strategies for this rare presentation.
  • To contribute to the limited literature on infantile extra-axial CPA medulloblastoma.

Main Methods:

  • Case report presentation.
  • Review of relevant medical literature.
  • Discussion of clinical presentation, diagnostic imaging, and treatment approaches.

Main Results:

  • An 8-month-old infant presented with an extra-axial CPA medulloblastoma.
  • The case highlights the rarity of this tumor location and age group.
  • Management strategies were considered based on available literature and clinical findings.

Conclusions:

  • Extra-axial CPA medulloblastoma, though rare, can occur in infants.
  • Early diagnosis and tailored management are crucial for favorable outcomes.
  • Further case reports are needed to better understand this rare pediatric brain tumor.

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