Catheter-based biopsy leading to early surgical intervention of the pulmonary artery intimal sarcoma

Pulmonary artery intimal sarcoma (PAIS) is an extremely rare disease that portends a dismal prognosis. To reach a diagnosis, several diagnostic measures are performed but pathological confirmation is required for an ultimate diagnosis. We report a case where a catheter-based, less invasive approach led to the diagnosis and curative intervention for PAIS. <Learning objective: Catheter-based biopsy could lead to early diagnosis of pulmonary artery intimal sarcoma and surgical intervention that would improve the outcome.>.