Bilateral auricular lymphoplasmacytic lymphoma: barely mere coincidence

Area of Science:

• Oncology
• Dermatology

Background:

• Lymphangioendotheliomatosis (LPL) is a rare neoplastic proliferation of lymphatic endothelial cells.
• Bilateral auricular involvement is an unprecedented presentation of LPL.

Observation:

• The patient presented with simultaneous LPL affecting both auricles as the sole initial manifestation.
• No significant systemic disease was detected, precluding the need for immunochemotherapy.

Findings:

• Radiation therapy, as a single modality, successfully induced a stable remission.
• The case suggests a potential localized pathogenesis for paired auricular lymphoma.

Implications:

• This case highlights the importance of considering rare cutaneous presentations for systemic diseases.
• Further research into the environmental and genetic factors influencing localized LPL is warranted.