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Heart Failure in a Child: Multimodality Approach Leading to an Unusual Cause
Uma Devi Karuru1, Jay Relan1, Mansi Verma2
1Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
JACC. Case Reports
|December 17, 2021
Insights
Isolated pulmonary artery vasculitis is a rare cause of heart failure in children. This case highlights severe pulmonary hypertension and artery stenosis in a 10-year-old due to this condition.
Area of Science:
- Pediatric Cardiology
- Pediatric Rheumatology
- Vascular Medicine
Background:
- Isolated pulmonary artery vasculitis is an uncommon condition, particularly in pediatric populations.
- Pulmonary artery vasculitis can lead to significant cardiopulmonary complications.
Observation:
- A 10-year-old child presented with symptoms of right heart failure.
- The patient exhibited severe pulmonary hypertension and bilateral branch pulmonary artery stenosis.
Findings:
- The child's condition was diagnosed as isolated pulmonary artery vasculitis.
- This vasculitis was the direct cause of the observed pulmonary hypertension and stenosis.
Implications:
- This case underscores the importance of considering rare vasculitides in pediatric heart failure.
- Early diagnosis and management of pulmonary artery vasculitis are crucial to prevent severe outcomes.
- Further research into pediatric pulmonary vasculitis is warranted.
Abstract:
Heart failure secondary to isolated pulmonary artery vasculitis is rarely described in children. We describe a 10-year-old child who presented with right heart failure symptoms, severe pulmonary hypertension, and bilateral branch pulmonary artery stenosis secondary to isolated pulmonary artery vasculitis. (Level of Difficulty: Advanced.).
Keywords:
ESR, erythrocyte sedimentation rateFDG-PET, fluorodeoxyglucose-positron emission tomographyLPA, left pulmonary arteryMPA, main pulmonary arteryPA, pulmonary arteryPPS, peripheral pulmonary artery stenosisRA, right atriumRPA, right pulmonary arteryRV, right ventricleTA, Takayasu arteritisTakayasu arteritiscongestive heart failureperipheral pulmonary artery stenosispulmonary artery interventionpulmonary artery vasculitis
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