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Published on: April 11, 2018
Cystic Fibrosis Foundation otolaryngology care multidisciplinary consensus recommendations
Adam J Kimple1, Brent A Senior1, Edward T Naureckas2
1Department of Otolaryngology/Head & Neck Surgery, The University of North Carolina, Chapel Hill, North Carolina, USA.
International Forum of Allergy & Rhinology
|January 28, 2022
Summary
Cystic fibrosis (CF) patients often need ear, nose, and throat care for conditions like chronic rhinosinusitis, hearing loss, and voice problems. This study provides consensus recommendations for managing these CF-related otolaryngologic symptoms.
Area of Science:
- Otolaryngology
- Pulmonology
- Genetics
Background:
- Cystic fibrosis (CF) is a multisystem disorder impacting multiple organ systems.
- Patients with CF frequently experience chronic rhinosinusitis, hearing loss, and dysphonia, necessitating otolaryngology care.
- Optimal management strategies for sinonasal, otologic, and laryngologic symptoms in CF patients lack established consensus.
Purpose of the Study:
- To develop multidisciplinary consensus recommendations for the otolaryngologic care of individuals with cystic fibrosis.
- To provide guidance on managing sinonasal, otologic, and laryngologic symptoms in CF patients.
- To establish a framework for optimal medical and surgical interventions for CF-related otolaryngologic conditions.
Main Methods:
- A multidisciplinary team, including CF Foundation experts and patients, was convened.
- Recommendations were developed based on a systematic literature review.
- A consensus of ≥80% was required for the adoption of recommendation statements.
Main Results:
- Twenty-five statements were voted on by the committee.
- Eleven statements recommending specific treatments or interventions were adopted.
- Eight statements were recommended as options for select patients, and five recommended against specific interventions.
Conclusions:
- Multidisciplinary consensus recommendations are established to guide otolaryngology consultation and management for CF patients.
- A collaborative approach is advocated for optimal care of individuals with CF.
- Future research should focus on standardized outcomes, modulator therapies, and genetic characteristics to advance CF care.
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