Congenital Pulmonary Airway Malformation in an Adult Male Presenting With Hemoptysis

Marcos Valentin1, Radhika Sharma1, Jorge Trabanco2

  • 1Internal Medicine, University of Florida College of Medicine - Jacksonville, Jacksonville, USA.

Cureus
|February 11, 2022
PubMed

Insights

Adults rarely develop congenital pulmonary airway malformations (CPAMs), but symptomatic cases require surgical resection for effective treatment and prevention of complications like bleeding.

Area of Science:

  • Pulmonology
  • Thoracic Surgery
  • Medical Case Reports

Background:

  • Congenital pulmonary airway malformations (CPAMs) are uncommon in adults, often remaining asymptomatic until later in life.
  • Adult CPAM presentation carries risks including infection, hemorrhage, pneumothorax, and potential malignancy.

Observation:

  • A case of an adult male presenting with significant hemoptysis due to a CPAM is detailed.
  • Diagnostic imaging (CT scan) and bronchoscopy confirmed the lesion's location in the lingula.

Findings:

  • The patient underwent successful elective surgical resection of the CPAM via video-assisted thoracoscopic surgery.
  • The procedure resulted in no adverse outcomes for the patient.

Implications:

  • Surgical resection is recommended as a safe and effective treatment for symptomatic adult CPAMs.
  • While interventions like tranexamic acid and embolization manage hemoptysis, they do not replace definitive surgical management due to recurrence risks.

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