A six-chambered heart: cor triatriatum sinister with double-chambered right ventricle in association with ventricular

Vivek Jaswal1, Pratyaksha Rana2, Vidur Bansal3

  • 1Department of Cardiothoracic and Vascular Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, 160012, India.

Insights

This study details a rare "6-chambered heart" case, combining cor triatriatum sinistrum (CTS) and double-chambered right ventricle (DCRV). Successful surgical repair was achieved, highlighting the importance of accurate diagnosis for complex congenital heart defects.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Pediatric Cardiac Surgery

Background:

  • Cor triatriatum involves atrial division by a membrane, creating three compartments.
  • Double-chambered right ventricle (DCRV) is characterized by an anomalous muscle bundle dividing the ventricle.

Purpose of the Study:

  • To describe an extremely rare case of combined cor triatriatum sinistrum (CTS) and DCRV.
  • To emphasize the implications of this combined anomaly on surgical repair.

Main Methods:

  • Case report of a pediatric patient with a complex congenital heart anomaly.
  • Description of successful intracardiac repair.

Main Results:

  • The patient presented with a unique "6-chambered heart" due to the coexistence of CTS and DCRV.
  • Successful surgical intervention was performed.

Conclusions:

  • The association of CTS with DCRV is exceptionally rare, creating a "6-chambered heart".
  • Accurate preoperative diagnosis is crucial for managing the complexities of surgical repair in such cases.
Abstract

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