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Published on: December 16, 2022
A six-chambered heart: cor triatriatum sinister with double-chambered right ventricle in association with ventricular
Vivek Jaswal1, Pratyaksha Rana2, Vidur Bansal3
1Department of Cardiothoracic and Vascular Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, 160012, India.
Insights
This study details a rare "6-chambered heart" case, combining cor triatriatum sinistrum (CTS) and double-chambered right ventricle (DCRV). Successful surgical repair was achieved, highlighting the importance of accurate diagnosis for complex congenital heart defects.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Pediatric Cardiac Surgery
Background:
- Cor triatriatum involves atrial division by a membrane, creating three compartments.
- Double-chambered right ventricle (DCRV) is characterized by an anomalous muscle bundle dividing the ventricle.
Purpose of the Study:
- To describe an extremely rare case of combined cor triatriatum sinistrum (CTS) and DCRV.
- To emphasize the implications of this combined anomaly on surgical repair.
Main Methods:
- Case report of a pediatric patient with a complex congenital heart anomaly.
- Description of successful intracardiac repair.
Main Results:
- The patient presented with a unique "6-chambered heart" due to the coexistence of CTS and DCRV.
- Successful surgical intervention was performed.
Conclusions:
- The association of CTS with DCRV is exceptionally rare, creating a "6-chambered heart".
- Accurate preoperative diagnosis is crucial for managing the complexities of surgical repair in such cases.
Background:
Cor triatriatum has been described as a heart with three atria in which the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is divided into two compartments by a fold of tissue, a membrane, or a fibromuscular band. Double-chambered right ventricle, on the other hand, is identified by the presence of an anomalous muscle bundle dividing the right ventricle into two chambers.
Case Presentation:
Here, we describe the case of a child who had a combination of both of these rare entities, effectively creating a heart with six chambers. The child underwent a successful intracardiac repair.
Conclusions:
The association of CTS with DCRV forming a "6-chambered heart" is extremely rare. Awareness of its existence and accurate preoperative diagnosis has important implications in its surgical repair with all the components of this disease spectrum, further increasing the complexity of a successful surgical repair.
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