Left Ventricular Enlargement Procedure in a Patient with Diffuse-Type Hypertrophic Cardiomyopathy: A Case Report

Dong Youb Han1, Sung Jun Park2, Sung-Ho Jung1

  • 1Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.

Journal of Chest Surgery
|February 22, 2022
PubMed

Insights

Surgical septal myectomy treats obstructive hypertrophic cardiomyopathy. A novel combined transaortic and transapical approach was used for left ventricular enlargement in a complex hypertrophic cardiomyopathy case.

Area of Science:

  • Cardiovascular Surgery
  • Cardiac Surgery
  • Hypertrophic Cardiomyopathy Research

Background:

  • Surgical septal myectomy is the gold standard for medically intractable obstructive hypertrophic cardiomyopathy.
  • Extended transaortic septal myectomy effectively addresses subaortic obstruction.
  • Transapical myectomy offers an alternative for specific hypertrophic cardiomyopathy phenotypes like apical hypertrophy.

Observation:

  • A patient presented with diffuse hypertrophic cardiomyopathy, apical aneurysm, and mid-cavity obstruction.
  • A combined transaortic and transapical dual surgical approach was employed.
  • This dual approach aimed to achieve left ventricular enlargement.

Findings:

  • The case demonstrates the feasibility of a combined transaortic and transapical approach.
  • This technique was utilized for left ventricular enlargement in a complex hypertrophic cardiomyopathy case.
  • The procedure addressed diffuse-type hypertrophic cardiomyopathy with apical aneurysm and mid-cavity obstruction.

Implications:

  • This combined approach may expand surgical options for complex hypertrophic cardiomyopathy.
  • It offers a potential solution for patients with challenging anatomical variations.
  • Further research could validate this dual-approach for similar challenging cases.

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