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A Rare Case of Dandy-Walker Syndrome
Mohammad Sharif Oria1, Aziz Rahman Rasib2, Ahmad Fawad Pirzad3
1Anesthesiology Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan.
International Medical Case Reports Journal
|February 25, 2022
Summary
Dandy-Walker syndrome (DWS), a congenital malformation, was treated in a 16-year-old female with a cystoperitoneal shunt. Surgical intervention improved her neurological symptoms, including unsteady gait and memory loss.
Area of Science:
- Neurology
- Pediatric Neurology
- Congenital Malformations
Background:
- Dandy-Walker syndrome (DWS) is a rare congenital brain malformation.
- It involves cerebellar vermis hypoplasia, upward rotation, and fourth ventricle enlargement.
- Clinical signs include psychomotor retardation, ataxia, and hydrocephalus.
Observation:
- A 16-year-old female presented with unsteady gait, memory deterioration, and urinary incontinence.
- Brain MRI confirmed DWS with a cystic posterior fossa and dilated fourth ventricles.
- The patient's parents provided informed consent for surgical intervention.
Findings:
- A cystoperitoneal (CP) shunt was surgically placed to address the DWS.
- Post-surgery, the patient showed improvement in her presenting clinical symptoms.
- The patient was discharged with enhanced neurological function.
Implications:
- This case highlights the successful surgical management of Dandy-Walker syndrome in an adolescent.
- Cystoperitoneal shunting can effectively alleviate symptoms associated with DWS.
- Early diagnosis and timely surgical intervention are crucial for better patient outcomes in DWS.
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