Eisenmenger syndrome with left main compression syndrome: a case report
Charlotte Johanna Cool1, Fathy Fathini2, Ibnu Adams3
1Congenital Heart Disease Division, Department of Cardiology and Vascular Medicine, University of Padjadjaran, Hasan Sadikin General Hospital, Jl. Pasteur No. 38, Bandung, 40161, Indonesia. charlotte@unpad.ac.id.
BMC Cardiovascular Disorders
|March 6, 2022
Summary
Eisenmenger syndrome can cause left main coronary artery compression, leading to angina. Prompt diagnosis and stenting offer a better quality of life for affected patients.
Area of Science:
- Cardiology
- Pulmonary Hypertension
- Interventional Cardiology
Background:
- Eisenmenger syndrome, a severe complication of uncorrected congenital heart disease, can lead to pulmonary artery dilation.
- Pulmonary artery dilation can compress the left main coronary artery, causing ischemic symptoms like angina.
- This condition is often underdiagnosed and mistaken for primary pulmonary hypertension symptoms.
Observation:
- A 37-year-old man with Eisenmenger syndrome presented with exertional angina.
- Cardiac CT revealed left main coronary artery compression due to a dilated pulmonary artery.
- The patient underwent successful IVUS-guided stent implantation in the left main coronary artery.
Findings:
- Successful stenting relieved angina symptoms and improved the patient's quality of life.
- Coronary angiography at 3 months showed good stent patency without restenosis.
- Left main coronary artery stenting is an effective emergent treatment for this condition.
Implications:
- Left main coronary artery compression should be suspected in Eisenmenger syndrome patients with angina.
- Early diagnosis via non-invasive imaging and coronary angiography is crucial.
- Stenting provides an ideal emergent treatment option, improving patient outcomes and quality of life.
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