Related Experiment Video
Updated: Oct 1, 2025
06:04
Systematic Hearing Performance Evaluation Process for Adolescents with Cochlear Implantation at Early Ages
Published on: March 24, 2023
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Cochlear Implant Outcomes in CHARGE Syndrome: Updated Perspectives
Emily Kay-Rivest1, Sean O McMenomey, Daniel Jethanamest
1Department of Otolaryngology - Head and Neck Surgery, NYU Grossman School of Medicine, New York, New York.
Summary
Auditory implants, including cochlear implants (CI) and auditory brainstem implants (ABI), show improved outcomes in children with CHARGE syndrome. Earlier and bilateral implantation is recommended for better hearing rehabilitation.
Area of Science:
- Otolaryngology
- Pediatric Audiology
- Genetics
Background:
- CHARGE syndrome presents complex audiological challenges.
- Hearing loss management in this population requires specialized approaches.
Purpose of the Study:
- To evaluate auditory implant outcomes in children with CHARGE syndrome.
- To describe the evolution of hearing loss management strategies.
Main Methods:
- Retrospective case review of children with CHARGE syndrome receiving cochlear implants (CI) or auditory brainstem implants (ABI).
- Analysis of clinical records, audiology, and rehabilitation interventions.
Main Results:
- Thirteen children received 19 implants; earlier and bilateral implantation increased.
- Improved subjective hearing assessments were noted post-implantation.
- One child with progressive hearing loss showed significant benefit.
Conclusions:
- Children with CHARGE syndrome benefit from earlier and bilateral auditory implantation.
- Cochlear implant evaluation is recommended to maximize auditory potential.
