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Hindgut Duplication in an Infant with Omphalocele-Exstrophy-Imperforate Anus-Spinal Defects (OEIS) Complex
Timothy F Tirrell1, Farokh R Demehri1, Craig W Lillehei1
1Department of Surgery, Boston Children's Hospital, Boston, Massachusetts, United States.
European Journal of Pediatric Surgery Reports
|March 14, 2022
Summary
This case report details a rare instance of OEIS complex (omphalocele, cloacal exstrophy, imperforate anus, and spinal abnormalities) co-occurring with fully duplicated hindguts in a neonate, highlighting a unique surgical approach.
Area of Science:
- Pediatric Surgery
- Congenital Anomalies
- Gastrointestinal Surgery
Background:
- Omphalocele, cloacal exstrophy, imperforate anus, and spinal abnormalities (OEIS) complex is a rare congenital anomaly.
- Hindgut duplications are uncommon and have not been previously associated with OEIS complex.
Observation:
- A neonate diagnosed with OEIS complex presented with fully duplicated, blind-ending hindguts.
- Surgical intervention involved closure of the omphalocele, separation of pelvic structures, and hindgut rescue.
Findings:
- Inspection revealed two distinct hindgut structures originating from the cecal plate, each with a separate mesentery.
- The duplicated hindguts were surgically unified to create a single lumen, aiming to maximize mucosal surface area.
Implications:
- This case highlights the co-occurrence of two rare anomalies and the surgical strategy for managing combined OEIS and hindgut duplications.
- Careful assessment of the hindgut is crucial during OEIS repair due to potential abnormalities.
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