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Degos disease complicated by constrictive pericarditis in remote phase: a case report

Yuki Tadokoro1, Tadashi Kitamura2, Tetsuya Horai2

  • 1Department of Cardiovascular Surgery, Kitasato University School of Medicine, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa, 252-0374, Japan. ss598yaeshio@gmail.com.

Journal of Cardiothoracic Surgery
|April 2, 2022
PubMed

Insights

Degos disease can lead to long-term constrictive pericarditis (CP). Aspirin helped manage the disease, but surgery was needed for heart failure unresponsive to treatment.

Area of Science:

  • Cardiology
  • Dermatology
  • Pathology

Background:

  • Degos disease, a rare condition causing skin issues via thrombo-obliterative vasculopathy, can rarely manifest as late-onset constrictive pericarditis (CP).
  • This case highlights CP developing 20 years after a Degos disease diagnosis.

Observation:

  • A 62-year-old woman with a 20-year history of Degos disease on aspirin presented with heart failure.
  • Diagnosis revealed constrictive pericarditis (CP); pericardiectomy was performed.
  • Pathological results indicated Degos disease involvement.

Findings:

  • Degos disease can be a long-term cause of constrictive pericarditis (CP).
  • Aspirin therapy demonstrated efficacy in inhibiting Degos disease progression.
  • Surgical intervention (pericardiectomy) proved necessary for refractory heart failure due to CP.

Implications:

  • This case underscores the potential for Degos disease to cause chronic cardiovascular complications.
  • Effective long-term management of Degos disease may involve aspirin and timely surgical consideration for CP.
  • Further research into the link between Degos disease and cardiovascular complications is warranted.
Abstract

Keywords:
Constrictive pericarditisDegos diseaseHeart failure

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