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Degos disease complicated by constrictive pericarditis in remote phase: a case report
Yuki Tadokoro1, Tadashi Kitamura2, Tetsuya Horai2
1Department of Cardiovascular Surgery, Kitasato University School of Medicine, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa, 252-0374, Japan. ss598yaeshio@gmail.com.
Journal of Cardiothoracic Surgery
|April 2, 2022
Summary
Degos disease can lead to long-term constrictive pericarditis (CP). Aspirin helped manage the disease, but surgery was needed for heart failure unresponsive to treatment.
Area of Science:
- Cardiology
- Dermatology
- Pathology
Background:
- Degos disease, a rare condition causing skin issues via thrombo-obliterative vasculopathy, can rarely manifest as late-onset constrictive pericarditis (CP).
- This case highlights CP developing 20 years after a Degos disease diagnosis.
Observation:
- A 62-year-old woman with a 20-year history of Degos disease on aspirin presented with heart failure.
- Diagnosis revealed constrictive pericarditis (CP); pericardiectomy was performed.
- Pathological results indicated Degos disease involvement.
Findings:
- Degos disease can be a long-term cause of constrictive pericarditis (CP).
- Aspirin therapy demonstrated efficacy in inhibiting Degos disease progression.
- Surgical intervention (pericardiectomy) proved necessary for refractory heart failure due to CP.
Implications:
- This case underscores the potential for Degos disease to cause chronic cardiovascular complications.
- Effective long-term management of Degos disease may involve aspirin and timely surgical consideration for CP.
- Further research into the link between Degos disease and cardiovascular complications is warranted.
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