Robotic treatment of ureteropelvic junction obstruction in Eagle-Barrett Syndrome
Lauren S Faber1, Julie M Riley2
1Department of Surgery (Division of Urology), University of New Mexico, Albuquerque, New Mexico, USA.
The Canadian Journal of Urology
|April 16, 2022
Abstract:
Eagle-Barrett Syndrome (EBS) is a rare congenital condition characterized by the triad of absent or defective abdominal wall muscles, urinary tract abnormalities, and bilateral cryptorchidism. Ureteropelvic junction obstruction (UPJO) is seldom reported in these patients, despite it being a common cause of childhood obstructive uropathy. We present the case of a patient with EBS who was subsequently identified as having symptomatic UPJO that was successfully treated with robotic pyeloplasty.
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