Rare case of mesocardia with ostium secundum ASD and double IVC

Shriram Kumar1, Shreyas Raghavan Nandyal1, Sharanya Kaushik2

  • 1Medicine, Gandhi Medical College and Hospital, Secunderabad, Hyderabad, Telangana, India.

BMJ Case Reports
|April 26, 2022
PubMed

Insights

This case report details an extremely rare instance of mesocardia, a congenital heart anomaly affecting 0.2% of individuals. The patient also presented with an atrial septal defect and a double inferior vena cava, highlighting the need for thorough cardiac anomaly workups.

Area of Science:

  • Cardiology
  • Medical Imaging
  • Pediatric Congenital Anomalies

Background:

  • Mesocardia is a rare congenital cardiac anomaly, occurring in approximately 0.2% of cases.
  • Congenital heart anomalies often present with associated cardiovascular abnormalities.
  • Early and accurate diagnosis is crucial for managing associated conditions and improving patient outcomes.

Observation:

  • A patient presented with symptoms suggestive of an atrial septal defect (ASD) with a left-to-right shunt, leading to pulmonary congestion and recurrent pneumonia.
  • Diagnostic workup revealed an extremely rare combination of mesocardia and a double inferior vena cava (IVC).

Findings:

  • The case highlights the co-occurrence of mesocardia with other congenital anomalies, specifically ASD and double IVC.
  • Thorough investigation uncovered these rare conditions, which were not the initial presenting diagnoses.
  • The patient's condition emphasized the importance of a comprehensive diagnostic approach for congenital cardiac anomalies.

Implications:

  • This case underscores the necessity of a meticulous workup for all congenital cardiac anomalies to identify associated vascular and cardiac conditions.
  • Recognizing rare combinations like mesocardia with double IVC can guide future diagnostic strategies.
  • Such detailed case reports contribute valuable data for understanding the spectrum and clinical significance of rare congenital heart diseases.

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