Cicatricial pemphigoid of upper digestive and respiratory tracts

Cicatricial pemphigoid can no longer be considered a "benign" bullous disorder. The most critical lesions are those involving the larynx and esophagus. Endoscopy, biopsy, and culture are essential as early in the patient's course as possible. Surgical intervention might include tracheostomy or gastrostomy and possibly surgical rehabilitation of the airway.