[Turner Syndrome Requiring Two Open Heart Surgeries:Report of a Case]

A 55-year-old woman was diagnosed with Turner syndrome following amenorrhea at age 20. Since then, hormone replacement therapy has been used in the obstetrics and gynecology department, but follow-up for cardiovascular disease has not been performed. At age 44, she was taken to our hospital for the first time because of acute aortic dissection and rupture, and urgently underwent total arch replacement. At age 55, she needed aortic valve and ascending aortic replacements for aortic regurgitation, ascending aortic aneurysm, and heart failure caused by the bicuspid aortic valve. Cardiovascular manifestation in Turner syndrome patients is common, and close follow-up using imaging studies may predict emergency diseases that critically affect patient's life. Medical professionals should inform patients and families of the value of follow-up.