Multimodality imaging of cor triatriatum dexter complicated with hypertrophic cardiomyopathy of restrictive phenotype

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Morphological and Functional Assessment of the Right Ventricle Using 3D Echocardiography
07:11

Morphological and Functional Assessment of the Right Ventricle Using 3D Echocardiography

Published on: October 28, 2020

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Li Liang1,2, Min-Jie Lu2

  • 1Department of Medical Image Center, Gansu Provincial Maternity and Child-care Hospital, North Road 143, Qilihe District, Lanzhou, 730000, China.

Radiology Case Reports
|June 6, 2022
PubMed

Insights

Cor triatriatum dexter (CTD), a rare heart defect, and hypertrophic cardiomyopathy (HCM) with a restrictive phenotype can coexist. This case highlights multimodal imaging for diagnosing this complex cardiac condition and guiding treatment.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Cardiomyopathy

Background:

  • Cor triatriatum dexter (CTD) is a rare congenital cardiac malformation characterized by a dividing membrane within the right atrium.
  • Hypertrophic cardiomyopathy (HCM) with a restrictive phenotype is an uncommon form of cardiomyopathy.

Observation:

  • A patient presented with an 18-year history of chest discomfort, fatigue, and syncope, particularly after intense physical activity.
  • This patient was diagnosed with a complex cardiac condition involving both CTD and HCM with a restrictive phenotype.

Findings:

  • Multimodal imaging was crucial in diagnosing this rare combination of CTD and restrictive HCM.
  • Imaging analysis identified the primary cause of the patient's heart failure.

Implications:

  • Accurate diagnosis through multimodal imaging is essential for effective clinical management of complex cardiac diseases like CTD with HCM.
  • This case provides valuable insights into the prognosis and treatment strategies for patients with this rare condition.

Keywords:
Cardiac magnetic resonance imagingCor triatriatum dexterHypertrophic cardiomyopathyRestrictive phenotype

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