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Case of Botryoid Rhabdomyosarcoma Mimicking Biliary Hydatid Disease
Suha Mohammad Akbar1, Harish Chandra Tudu2, Subrat Kumar Mohanty3
1Department of Surgery, KIMS, Bhubaneswar, Odisha, India.
Insights
Hepatobiliary rhabdomyosarcoma, a rare childhood biliary tract cancer, can mimic benign conditions. This case highlights its unusual presentation in a young child with obstructive jaundice and atypical imaging.
Area of Science:
- Pediatric Oncology
- Hepatobiliary Surgery
- Pediatric Pathology
Background:
- Hepatobiliary rhabdomyosarcoma (RMS) is a rare malignant soft tissue tumor originating in the biliary tract.
- This condition predominantly affects children and often presents with symptoms mimicking common benign biliary diseases.
- The rarity and atypical presentation can pose diagnostic challenges.
Abstract:
Hepatobiliary rhabdomyosarcoma (RMS) is a soft tissue malignant musculoskeletal tumor of the biliary tract. It is rare tumor, mostly seen in children and mimics common benign biliary condition. Here, we present a case of 1 year 9 months child of biliary RMS who presented with obstructive jaundice and diagnosed after biopsy. This case highlights the unusual childhood malignancy of bile duct RMS in obstructive jaundice with atypical imaging findings.

