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[Bluish cutaneo-digestive angiomatosis or Bean's blue rubber-bleb nevus. A rare syndrome]
Abstract:
A 13 years old girl is admitted for severe chronic anemia. Few blood sac looking like lesion are discovered. A Blue Rubber Bleb Nevus Syndrome is confirmed discovery of multiple intestinal angioma. No deep lesion is discovered otherwise. Clinical characteristics, nosology and evolutive trend of this rare syndrome are recalled.