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Published on: July 18, 2014
Supracardiac Total Anomalous Pulmonary Venous Return Repair in a 7-Month-Old Infant
Mislav Planinc1, Ivan Malcic2, Darko Anic1
1Department of Congenital Heart Surgery, University Hospital Center Zagreb, Zagreb, Croatia.
Insights
Total anomalous pulmonary venous return (TAPVR) is a severe congenital heart defect. This case highlights a rare infant survival to 7 months with atypical TAPVR, followed by successful surgical repair and long-term recovery.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Total anomalous pulmonary venous return (TAPVR) is a critical congenital heart malformation.
- Pulmonary veins abnormally connect to the right atrium, necessitating early surgical intervention.
- Survival beyond infancy without surgical repair is exceedingly rare.
Purpose of the Study:
- To report an unusual case of supracardiac TAPVR in an infant.
- To describe the management of a patient with atypical venous return and ductal shunting.
- To highlight successful surgical outcomes in a complex pediatric cardiac case.
Main Methods:
- Case report of an infant with supracardiac TAPVR.
- Management involved stabilization of left heart function.
- Surgical repair of anomalous venous return was performed at 7 months of age.
Main Results:
- The infant survived for 7 months with atypical TAPVR and right-to-left shunting via a patent ductus arteriosus.
- Surgical repair was successfully performed 2 months after initial stabilization.
- The patient remained well with no complications 3 years post-surgery.
Conclusions:
- This case demonstrates the possibility of extended survival in infants with complex TAPVR.
- Early stabilization and timely surgical intervention are crucial for favorable outcomes.
- Successful surgical repair can lead to long-term recovery in challenging pediatric cardiac cases.
Abstract:
Total anomalous pulmonary venous return is a congenital heart malformation characterized by anomalous pulmonary venous inflow to the right atrium. Surgical repair typically occurs during the first month of life, and survival beyond that age in untreated patients is unlikely. We report an extreme case of supracardiac total anomalous pulmonary venous return in an infant who survived 7 months despite atypical anomalous inflow without atrial-level communication and with right-to-left shunting only through a patent ductus arteriosus. We stabilized the patient's left-sided heart function before surgically repairing the anomalous venous return 2 months later. Three years postoperatively, the patient was well.
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