Supracardiac Total Anomalous Pulmonary Venous Return Repair in a 7-Month-Old Infant

Mislav Planinc1, Ivan Malcic2, Darko Anic1

  • 1Department of Congenital Heart Surgery, University Hospital Center Zagreb, Zagreb, Croatia.

Insights

Total anomalous pulmonary venous return (TAPVR) is a severe congenital heart defect. This case highlights a rare infant survival to 7 months with atypical TAPVR, followed by successful surgical repair and long-term recovery.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Cardiac Surgery

Background:

  • Total anomalous pulmonary venous return (TAPVR) is a critical congenital heart malformation.
  • Pulmonary veins abnormally connect to the right atrium, necessitating early surgical intervention.
  • Survival beyond infancy without surgical repair is exceedingly rare.

Purpose of the Study:

  • To report an unusual case of supracardiac TAPVR in an infant.
  • To describe the management of a patient with atypical venous return and ductal shunting.
  • To highlight successful surgical outcomes in a complex pediatric cardiac case.

Main Methods:

  • Case report of an infant with supracardiac TAPVR.
  • Management involved stabilization of left heart function.
  • Surgical repair of anomalous venous return was performed at 7 months of age.

Main Results:

  • The infant survived for 7 months with atypical TAPVR and right-to-left shunting via a patent ductus arteriosus.
  • Surgical repair was successfully performed 2 months after initial stabilization.
  • The patient remained well with no complications 3 years post-surgery.

Conclusions:

  • This case demonstrates the possibility of extended survival in infants with complex TAPVR.
  • Early stabilization and timely surgical intervention are crucial for favorable outcomes.
  • Successful surgical repair can lead to long-term recovery in challenging pediatric cardiac cases.