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Hypertrophic cardiomyopathy. Proposal for a new classification

Guillermo A Llamas-Esperón1, Guillermo Llamas-Delgado2

  • 1Leadership of the Department of Interventional Cardiology.

Archivos De Cardiologia De Mexico
|June 30, 2022
PubMed

Insights

Hypertrophic cardiomyopathy (HCM) has been known by over 75 names due to its complex nature. This study reviews HCM nomenclature and proposes a new classification for better diagnosis and treatment.

Area of Science:

  • Cardiology
  • Genetics
  • Pathology

Background:

  • Hypertrophic cardiomyopathy (HCM) presents significant diagnostic and therapeutic challenges due to its heterogeneous morphology and function.
  • The condition has historically been known by over 75 different names, complicating consistent understanding and management.
  • Echocardiographic classification of HCM has been difficult for over 40 years.

Purpose of the Study:

  • To review the historical nomenclature of hypertrophic cardiomyopathy.
  • To propose a novel classification system for HCM.
  • To enhance clinical and surgical cardiologists' understanding of HCM's diverse aspects.

Main Methods:

  • Comprehensive literature review of HCM nomenclature and classification systems.
  • Analysis of morphological and functional heterogeneity in HCM.
  • Development of a proposed new classification framework.

Main Results:

  • Identified over 75 historical names for hypertrophic cardiomyopathy.
  • Highlighted the persistent challenges in diagnosing and classifying HCM.
  • Proposed a new classification aimed at improving clinical and surgical management.

Conclusions:

  • A unified and practical classification is crucial for understanding HCM's clinical behavior and prognosis.
  • The proposed classification aims to simplify the approach to HCM diagnosis and treatment.
  • Standardizing HCM terminology and classification will benefit patient care and research.

Keywords:
CardiomyopathiesClasificaciónClassificationHypertrophic cardiomyopathyMiocardiopatía hipertróficaMiocardiopatías

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