Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

[Primary fibrosing cholangitis (author's transl)].

E Roseau

    La Nouvelle Presse Medicale
    |August 2, 1978
    PubMed
    Summary

    Primary fibrosing cholangitis is a rare, severe biliary disorder characterized by inflammatory stenosis. Current treatments for this condition can only delay its fatal progression.

    Related Concept Videos

    You might also read

    Related Articles

    Articles linked to this work by shared authors, journal, and citation graph.

    Sort by
    Same author

    [Vesico-ureteral reflux and nephropathy in the child: medical or surgical treatment?].

    Presse medicale (Paris, France : 1983)·2001
    Same author

    [ABO-incompatible heart transplantation in infants].

    Presse medicale (Paris, France : 1983)·2001
    Same author

    [Cancer of the rectum: contribution of MRI in predicting complete resection].

    Presse medicale (Paris, France : 1983)·2001
    Same author

    [Metastatic nephrocarcinoma: regression after peripheral lymphocyte transplantation from compatible donors].

    Presse medicale (Paris, France : 1983)·2001
    Same author

    [Crohn's disease: prevention of relapse with methotrexate or growth hormone].

    Presse medicale (Paris, France : 1983)·2000
    Same author

    [Liver transplantation: the problem of peroperative bleeding].

    Presse medicale (Paris, France : 1983)·2000

    Area of Science:

    • Hepatology
    • Gastroenterology
    • Pathology

    Context:

    • Primary fibrosing cholangitis is a rare and severe disorder affecting the biliary system.
    • It involves inflammatory stenosis of the extrahepatic or intrahepatic bile ducts.
    • Histological features include intramural fibrous thickening with intact mucosa and serosa.

    Purpose:

    • To describe the characteristics and clinical presentation of primary fibrosing cholangitis.
    • To differentiate it from similar conditions like primary biliary cirrhosis.
    • To discuss the limited efficacy of current therapeutic interventions.

    Summary:

    • Primary fibrosing cholangitis presents as localized or extensive inflammatory stenosis of the bile ducts.
    • It shares similarities with primary biliary cirrhosis, suggesting a common response to an unknown etiological agent.
    • Surgical interventions such as stenosis resection or bypass procedures offer only palliative benefits, delaying inevitable fatal cholangitis.

    Impact:

    • Highlights the grave nature and diagnostic challenges of primary fibrosing cholangitis.
    • Underscores the need for further research into the etiology and effective treatments for this rare disease.
    • Informs clinical management by clarifying the limited scope of current surgical options.

    Related Experiment Videos