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Updated: Sep 4, 2025
Comprehensive Endovascular and Open Surgical Management of Cerebral Arteriovenous Malformations
Published on: October 20, 2017
Removal of malformation in cerebral proliferative angiopathy: illustrative case
Gwang Yoon Choi1, Hyuk Jai Choi1, Jin Pyeong Jeon1
1Department of Neurosurgery, Hallym University Chuncheon Sacred Heart Hospital, Chuncheon, Gangwon, Republic of Korea.
Background:
Cerebral proliferative angiopathy (CPA) is a rare vascular disorder distinct from arteriovenous malformation. Because of the disorder's rarity, there is still a controversy on the most promising treatment method for CPA. However, several meta-analysis articles suggest indirect vascularization such as encephalo-duro-arterio-synangiosis as an effective way of treating symptoms that are medically uncontrolled.
Observations:
The authors describe a case of an 11-year-old boy with this disease, who had epilepsy that was intractable despite conservative management. The patient recovered from his symptoms after the vascular malformation was surgically removed. This is the first reported case of surgical removal in CPA.
Lessons:
Although further investigation on the best treatment for CPA is needed, the authors believe surgical intervention may also be an effective treatment modality when a patient presents with persisting symptoms.
