Primary Wilms tumor of the urinary bladder
Mayur Parkhi1, Srinivasan Peyam2, Nitin James Peters3
1Post Graduate Institute and Medical Education and Research, Department of Histopathology, Chandigarh, India.
Autopsy & Case Reports
|August 3, 2022
Summary
Extrarenal Wilms tumor (ERWT) can rarely present in the urinary bladder. This case highlights the importance of considering ERWT in pediatric patients with bladder masses.
Area of Science:
- Pediatric Oncology
- Uropathology
Background:
- Wilms tumor (WT) typically arises in the kidney but can occur at extrarenal sites.
- Primary urinary bladder Wilms tumor is an uncommon presentation.
Observation:
- A 4-year-old female presented with micturition difficulties.
- Imaging revealed a bladder mass; biopsy confirmed triphasic extrarenal Wilms tumor (ERWT).
Findings:
- The patient underwent chemotherapy and partial cystectomy for residual tumor.
- Diagnosis of ERWT was confirmed, with the patient remaining well post-treatment.
Implications:
- Primary bladder WT should be considered in the differential diagnosis of pediatric small blue round cell tumors.
- Early and accurate diagnosis from biopsy is crucial for effective management and prognosis.
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