Anterior encephalocele presenting as nasolacrimal obstruction

A case of congenital anterior encephalocele presented originally with nasolacrimal obstruction. Associated paranasal masses and hypertelorism suggested the diagnosis, which was confirmed and delineated by computed tomography. Anterior encephalocele has various clinical presentations, but the diagnosis should be suspected in a child with nasolacrimal obstruction and associated congenital anomalies, particularly paranasal masses. Early recognition is essential to prevent trauma to CNS tissue, to prompt evaluation for other congenital anomalies, and to facilitate appropriate neurosurgical repair.