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Wolf in sheep's clothing: Primary orbital Ewing sarcoma in a child masquerading as internal angular dermoid
Teena Mariet Mendonca1, Harsha Prasada Lashkari2, Pooja K Suresh3
1Department of Ophthalmology, Kasturba Medical College, Mangalore Manipal Academy of Higher Education Manipal, Kozhikode, Kerala, India.
Oman Journal of Ophthalmology
|August 8, 2022
Summary
Primary orbital Ewing sarcoma is a rare and aggressive neuroectodermal tumor. Early diagnosis is crucial for this challenging condition, often presenting as a deceptive orbital mass.
Area of Science:
- Oncology
- Ophthalmology
- Pediatric Oncology
Background:
- Ewing sarcoma is a rare, highly malignant neuroectodermal tumor predominantly affecting bones.
- Primary involvement of the orbit by Ewing sarcoma is exceptionally rare.
Observation:
- A 5-year-old boy presented with a painless, slow-growing mass near the inner corner of his left eye.
- The clinical presentation mimicked a common benign lesion, an internal angular dermoid.
Findings:
- The patient was diagnosed with primary orbital Ewing sarcoma.
- This rare orbital tumor presents significant diagnostic challenges.
Implications:
- Primary orbital Ewing sarcoma has a poor prognosis.
- A high index of clinical suspicion is necessary for timely diagnosis and management of this rare pediatric malignancy.
