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Myocardial disturbances of intermediary metabolism in Barth syndrome

Amanda A Greenwell1,2, Seyed Amirhossein Tabatabaei Dakhili1,2, John R Ussher1,2

  • 1Faculty of Pharmacy and Pharmaceutical Sciences, University of Alberta, Edmonton, AB, Canada.

Frontiers in Cardiovascular Medicine
|August 29, 2022
PubMed

Keywords:
Barth syndrome (BTHS)cardiac energeticscardiomyopathyfatty acid oxidationglucose oxidationketone oxidation

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