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Electrophysiological Motor Unit Number Estimation MUNE Measuring Compound Muscle Action Potential CMAP in Mouse Hindlimb Muscles
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Motoneuron Diseases

Francesco Lotti1, Serge Przedborski2

  • 1Departments of Neurology, Pathology & Cell Biology, and Neuroscience, College of Physicians and Surgeons, Columbia University, New York, NY, USA.

Advances in Neurobiology
|September 6, 2022
PubMed

Keywords:
Amyotrophic lateral sclerosisC9ORF72Cell autonomyFUSMotoneuron diseasesMotor cortexNeurodegenerationSpinal cordSpinal muscular atrophySuperoxide dismutase-1TDP43

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