[Arrhythmogenic right ventricular cardiomyopathy : An update].

Area of Science:

• Cardiology
• Genetics
• Pathology

Background:

• Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a primary inherited myocardial disease.
• ARVC affects the right ventricle primarily, but can involve the left ventricle.
• It significantly increases the risk of ventricular arrhythmias, heart failure, and sudden cardiac death.

Purpose of the Study:

• To outline the diagnostic challenges and criteria for ARVC.
• To detail the essential components of patient-tailored management strategies for ARVC.
• To emphasize the importance of early diagnosis and appropriate interventions.

Main Methods:

• Diagnosis is based on established task-force criteria.
• Criteria include structural abnormalities (echocardiography, cardiac MRI), ECG findings, ventricular arrhythmias, histology, and family history.
• Management strategies are tailored to individual patient risk factors.

Main Results:

• Diagnosis of ARVC remains challenging, necessitating adherence to comprehensive criteria.
• Risk stratification guides the need for implantable cardioverter-defibrillator (ICD) implantation.
• Lifestyle modifications, including avoiding high-intensity physical activity, are crucial.

Conclusions:

• Effective management of ARVC requires a multi-faceted approach.
• Implantable cardioverter-defibrillators are indicated for high-risk patients.
• Beta-blockers and physical activity restrictions are key components of ARVC care.