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Updated: Aug 28, 2025
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Endoscopic Septoplasty with Limited Two-line Resection: Minimally Invasive Surgery for Septal Deviation
Published on: June 20, 2018
16.9K
Paediatric paranasal sinus fibrous dysplasia
A A Adeyemo1,2, S A Ogunkeyede2,3, A Daniel2,3
1Institute of Child Health, College of Medicine, University of Ibadan, Ibadan, Nigeria.
Tropical Doctor
|September 16, 2022
Summary
Delayed presentation of fibrous dysplasia in children often leads to extensive surgery and poor outcomes. Early diagnosis and intervention are crucial for better management of this rare developmental tumor affecting facial bones.
Area of Science:
- Oral and Maxillofacial Surgery
- Pediatric Oncology
- Developmental Biology
Background:
- Fibrous dysplasia of the paranasal sinuses is a rare developmental tumor.
- It can cause significant facial deformity and complications due to delayed presentation.
- Late diagnosis impacts surgical techniques and patient outcomes.
Purpose of the Study:
- To investigate factors contributing to delayed hospital presentation of pediatric fibrous dysplasia.
- To evaluate the management outcomes in relation to presentation delay.
- To identify trends in treatment and recurrence.
Main Methods:
- Retrospective review of 43 pediatric cases (1997-2018).
- Analysis of patient demographics, affected sites, surgical interventions, and follow-up data.
- Histological examination for tumor characteristics.
Main Results:
- Maxillary bones were the most commonly affected site.
- Surgical resection achieved good outcomes, with maxillectomy being an exception.
- Tumor recurrence occurred in five patients, despite the absence of mitotic cells on histology.
- Late presentation with complications was a common feature.
Conclusions:
- Delayed presentation of pediatric fibrous dysplasia is associated with poorer surgical outcomes.
- Effective health education is necessary to encourage earlier diagnosis and intervention.
- Further research into the biological behavior and optimal management strategies is warranted.
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