[Emergent Operation for Total Anomalous Pulmonary Venous Return].

Area of Science:

• Cardiology
• Pediatric Surgery
• Congenital Heart Disease

Background:

• Total anomalous pulmonary venous return with pulmonary venous obstruction is a severe congenital heart defect requiring immediate neonatal surgery.
• Patients present with critical lung congestion and pulmonary hypertension, necessitating prompt intervention for survival.

Purpose of the Study:

• To summarize typical surgical approaches and anastomosis techniques for creating a connection between the common pulmonary venous chamber and the left atrium.
• To review necessary perioperative treatments, including nitric oxide and open chest management.
• To reference early surgical outcomes using the Japanese National Clinical Database.

Main Methods:

• Review of typical surgical approaches and anastomosis techniques for total anomalous pulmonary venous return with obstruction.
• Description of perioperative management strategies.
• Analysis of early surgical outcomes from the Japanese National Clinical Database.

Main Results:

• The article summarizes standard surgical techniques for establishing pulmonary venous-left atrial connection.
• Perioperative management strategies like nitric oxide and open chest are discussed.
• Early surgical outcomes data from Japan are presented.

Conclusions:

• Surgical relief of pulmonary venous obstruction in total anomalous pulmonary venous return is essential for neonatal survival.
• Standardized surgical techniques and appropriate perioperative care are crucial for successful outcomes.
• The Japanese National Clinical Database provides valuable insights into early surgical results.